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结缔组织病相关肺动脉高压的研究进展分析

谢 培莉, 刘慧 慧*

摘要

结缔组织病是一组多系统、多器官受累的慢性系统性自身免疫病,该病可合并多种疾病,其中肺动脉高压是导致
结缔组织病患者死亡的重要原因之一。近年来,结缔组织病相关的肺动脉高压引起了世界的广泛关注。由于其临床表现隐匿,
不易发现,且发病机制尚不明确,故常会被忽略。本文关于结缔组织病伴肺动脉的发病机制、临床特点、治疗做一论述。

关键词

结缔组织病;肺动脉高压;发病机制;临床表现;治疗

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参考

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