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肝脏未分化胚胎性肉瘤临床病理分析及文献复习

陈 安敏, 史 连国, 方 庆全, 李宁 波*

摘要

目的 : 探讨肝脏未分化胚胎性肉瘤的临床表现、影像学征象、诊断、鉴别诊断、分子遗传特征及预后。方法 : 回顾
性分析本院确诊为未分化胚胎性肉瘤 2 例的临床病理资料,并复习相关文献。结果 : 两名患者均为女性,年龄 15-27 岁,
平均年龄 21 岁,肿瘤均位于肝右叶,镜下肿瘤细胞呈梭形、上皮样、多边形及瘤巨细胞样改变;可见较多量大小不等的嗜
酸性小体。免疫组化表达上皮源性标记、Vimentin 及 α1-AAT;嗜酸性小体 PAS 阳性。结论 : 肝脏未分化胚胎性肉瘤是一
种高度恶性肿瘤,术前影像学较难诊断,容易误诊,需病理及免疫组明确确诊。

关键词

肝脏未分化胚胎性肉瘤;肝细胞癌;临床病理;鉴别诊断;预后

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参考

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