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成人先天性巨结肠并乙状结肠扭转一例报道并文献复习

肖 寅峰, 刘 悦, 张 丽静

摘要

先天性巨结肠是一种先天性肠动力障碍性疾病,由于肠道的神经系统发育异常,引起远端结肠
脊髓丛、黏膜下丛神经元缺失,造成肠内容物积聚于无神经元肠段,引起慢性便秘、腹胀等症状。该疾病常诊
断于新生儿期,但它也可能出现在婴儿期、儿童期,甚至成年期。其中乙状结肠扭转是先天性巨结肠的一种罕
见并发症。因此,本文回顾性分析 1 例成人先天性巨结肠并乙状结肠扭转的临床病例资料,同时总结相关文献
报道,进一步提高临床医师对该疾病的认识。

关键词

成人;先天性巨结肠;乙状结肠扭转

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